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A febrile epileptic status in a child: FIRES syndrome. A case report
- Authors: Shatalin A.V.1, Kotov A.S.1, Borisova M.N.1, Panteleeva M.V.1, Matyuk Y.V.1, Romanova M.V.1, Kurysheva I.Y.1, Razheva I.V.2
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Affiliations:
- Vladimirsky Moscow Regional Research Clinical Institute, Moscow
- Somatic Department № 2, Children’s Hospital, Lyubertsy District Hospital № 3, Lyubertsy, Moscow Region
- Issue: Vol 10, No 1 (2016)
- Pages: 53-56
- Section: Original articles
- URL: https://annaly-nevrologii.com/journal/pathID/article/view/69
- DOI: https://doi.org/10.17816/psaic69
- Cite item
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Abstract
The article describes a clinical case of severe childhood epileptic syndrome, FIRES (DESC) syndrome, which is a form of epileptic encephalopathy in school-age children caused by hyperthermia. The emergence of this severe childhood condition leads to involvement of all diagnostic and human resources available at a pediatric critical care clinic to identify and treat this form of epileptic paroxysm. The described clinical case also had a severe course with a prolonged epileptic status, which was resistant to antiepileptic pharmacotherapy, and hyperthermia. The presented case is a modest contribution to the treasury of information about this syndrome in our country, with the aim to increase the doctors’ awareness of the problem.
Keywords
About the authors
A. V. Shatalin
Vladimirsky Moscow Regional Research Clinical Institute, Moscow
Author for correspondence.
Email: platonova@neurology.ru
Russian Federation
A. S. Kotov
Vladimirsky Moscow Regional Research Clinical Institute, Moscow
Email: platonova@neurology.ru
Russian Federation
M. N. Borisova
Vladimirsky Moscow Regional Research Clinical Institute, Moscow
Email: platonova@neurology.ru
Russian Federation
M. V. Panteleeva
Vladimirsky Moscow Regional Research Clinical Institute, Moscow
Email: platonova@neurology.ru
Russian Federation
Yu. V. Matyuk
Vladimirsky Moscow Regional Research Clinical Institute, Moscow
Email: platonova@neurology.ru
Russian Federation
M. V. Romanova
Vladimirsky Moscow Regional Research Clinical Institute, Moscow
Email: platonova@neurology.ru
Russian Federation
I. Yu. Kurysheva
Vladimirsky Moscow Regional Research Clinical Institute, Moscow
Email: platonova@neurology.ru
Russian Federation
I. V. Razheva
Somatic Department № 2, Children’s Hospital, Lyubertsy District Hospital № 3, Lyubertsy, Moscow Region
Email: platonova@neurology.ru
Russian Federation
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