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A febrile epileptic status in a child: FIRES syndrome. A case report
- Authors: Shatalin A.V.1, Kotov A.S.1, Borisova M.N.1, Panteleeva M.V.1, Matyuk Y.V.1, Romanova M.V.1, Kurysheva I.Y.2, Razheva I.V.3
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Affiliations:
- Vladimirsky Moscow Regional Research Clinical Institute
- Somatic Department No 2, Children’s Hospital, Lyubertsy District Hospital No 3
- Somatic Department № 2, Children’s Hospital, Lyubertsy District Hospital № 3
- Issue: Vol 10, No 1 (2016)
- Pages: 53-56
- Section: Clinical analysis
- URL: https://annaly-nevrologii.com/journal/pathID/article/view/69
- DOI: https://doi.org/10.17816/psaic69
- ID: 69
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Abstract
The article describes a clinical case of severe childhood epileptic syndrome, FIRES (DESC) syndrome, which is a form of epileptic encephalopathy in school-age children caused by hyperthermia. The emergence of this severe childhood condition leads to involvement of all diagnostic and human resources available at a pediatric critical care clinic to identify and treat this form of epileptic paroxysm. The described clinical case also had a severe course with a prolonged epileptic status, which was resistant to antiepileptic pharmacotherapy, and hyperthermia. The presented case is a modest contribution to the treasury of information about this syndrome in our country, with the aim to increase the doctors’ awareness of the problem.
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About the authors
A. V. Shatalin
Vladimirsky Moscow Regional Research Clinical Institute
Email: alex-013@yandex.ru
Russian Federation, Moscow
A. S. Kotov
Vladimirsky Moscow Regional Research Clinical Institute
Email: alex-013@yandex.ru
Russian Federation, Moscow
M. N. Borisova
Vladimirsky Moscow Regional Research Clinical Institute
Email: alex-013@yandex.ru
Russian Federation, Moscow
M. V. Panteleeva
Vladimirsky Moscow Regional Research Clinical Institute
Email: alex-013@yandex.ru
Russian Federation, Moscow
Yu. V. Matyuk
Vladimirsky Moscow Regional Research Clinical Institute
Email: alex-013@yandex.ru
Russian Federation, Moscow
M. V. Romanova
Vladimirsky Moscow Regional Research Clinical Institute
Email: alex-013@yandex.ru
Russian Federation, Moscow
I. Yu. Kurysheva
Somatic Department No 2, Children’s Hospital, Lyubertsy District Hospital No 3
Email: alex-013@yandex.ru
Russian Federation, Lyubertsy, Moscow Region
I. V. Razheva
Somatic Department № 2, Children’s Hospital, Lyubertsy District Hospital № 3
Author for correspondence.
Email: alex-013@yandex.ru
Russian Federation, Lyubertsy, Moscow Region
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СМИ зарегистрировано Федеральной службой по надзору в сфере связи, информационных технологий и массовых коммуникаций (Роскомнадзор).